Membranous Septal Aneurysm: An Unusual Cause for Right Ventricular Outflow Tract Obstruction in a Malaligned Ventricular Septal Defect with Aortomitral Discontinuity (Double-Outlet Right Ventricle) Associated with Visceral Heterotaxy

2008 ◽  
Vol 30 (2) ◽  
pp. 200-202 ◽  
Author(s):  
Sasidharan Bijulal ◽  
Sivasubramanian Sivasankaran ◽  
Ganapathy Sanjay ◽  
Jaganmohan Tharakan
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Right Ventricular ◽  
Septal Defect ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Double Outlet Right Ventricle ◽  
Outflow Tract ◽  
Ventricular Outflow Tract Obstruction ◽  
Visceral Heterotaxy

scholarly journals Unruptured Sinus of Valsalva Aneurysm with Right Ventricular Outflow Tract Obstruction and Supracristal Ventricular Septal Defect: A Rare Case

2015 ◽  
Vol 42 (5) ◽  
pp. 462-464
Author(s):  
Ganiga Srinivasaiah Sridhar ◽  
Muhammad Athar Sadiq ◽  
Wan Azman Wan Ahmad ◽  
Chitra Supuramaniam ◽  
Timothy Watson ◽  
...  
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricular ◽  
Septal Defect ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Outflow Tract ◽  
Sinus Of Valsalva ◽  
Exertional Dyspnea ◽  
Sinus Of Valsalva Aneurysm ◽  
Ventricular Outflow Tract Obstruction

Unruptured right sinus of Valsalva aneurysm that causes severe obstruction of the right ventricular outflow tract is extremely rare. We describe the case of a 47-year-old woman who presented with exertional dyspnea. Upon investigation, we discovered an unruptured right sinus of Valsalva aneurysm with associated right ventricular outflow tract obstruction and a supracristal ventricular septal defect. To our knowledge, only 2 such cases have previously been reported in the medical literature. Although treatment of unruptured sinus of Valsalva aneurysm remains debatable, surgery should be considered for extremely large aneurysms or for progressive enlargement of the aneurysm on serial evaluation. Surgery was undertaken in our patient because there was clear evidence of right ventricular outflow tract obstruction, right-sided heart dilation, and associated exertional dyspnea.

Transaortic Fallot repair in a grown-up patient: advantages in a situs inversus setting

2012 ◽  
Vol 22 (5) ◽  
pp. 603-605 ◽  
Author(s):  
Juan-Miguel Gil-Jaurena ◽  
Joaquín Cano ◽  
Victorio Cuenca
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricular ◽  
Situs Inversus ◽  
Septal Defect ◽  
Right Ventricular Outflow Tract ◽  
Heart Association ◽  
Ventricular Outflow Tract ◽  
Outflow Tract ◽  
Complete Relief ◽  
Ventricular Outflow Tract Obstruction

AbstractWe present the case studies of two adult patients with tetralogy of Fallot who were scheduled for surgery. After addressing the right ventricular outflow tract obstruction, the aorta was opened and the ventricular septal defect was approached in a straightforward manner as it was located just under the overriding aortic valve. The second patient presented with was a situs inversus, dextroapex Fallot. In this setting, the aortic approach simplified the repair expeditiously. After 2 years, both patients are in New York Heart Association class I, with no residual ventricular septal defect, no aortic regurgitation, and complete relief of right ventricular outflow tract obstruction.

Initial clinical manifestations and mid- and long-term results after surgical repair of double-chambered right ventricle in children and adults

2008 ◽  
Vol 18 (3) ◽  
pp. 268-274 ◽  
Author(s):  
Ragiab Telagh ◽  
Vladimir Alexi-Meskishvili ◽  
Ronald Hetzer ◽  
Peter E. Lange ◽  
Felix Berger ◽  
...  
Keyword(s):  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Right Ventricular ◽  
Septal Defect ◽  
Surgical Repair ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Outflow Tract ◽  
The Right

AbstractObjectiveBy means of retrospective analysis of our institutional experience, we reviewed the clinical manifestation and outcomes of patients subsequent to surgical repair of double-chambered right ventricle.MethodsBetween 1988 and 2005, we performed surgical repair in 35 of 37 patients diagnosed with double-chambered right ventricle. The patients ranged in age from 4 to 69 years, with a mean of 21.3 years. Most presented in infancy, with initial manifestation of a short systolic murmur in 34 (92%) of all cases. Pressure gradients were measured invasively across the right ventricular outflow tract of between 30 and 140 mmHg, with a median of 60 mmHg. An associated ventricular septal defect was present in 26 patients (70%). Of the group, 4 patients were aged over 40 years, and 2 had previously undergone operative closure of a ventricular septal defect.ResultsThe operative interval ranged from 2 months to 41 years, with a median of 9 years. In all, we resected muscular bundles and enlarged the right ventricular outflow tract. There was no hospital or late death. Median follow-up subsequent to surgery was 7 years, with a range from 0.4 to 11 years. No patient required further surgery to relieve any obstruction of the right ventricular outflow tract, nor long term medical therapy or pacing because of cardiac arrhythmia.ConclusionsSurgical repair of a double-chambered right ventricle yields excellent haemodynamic and functional results over the mid to long term.

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