Surgical therapy of Ebstein's anomaly in adulthood – from valve repair to heart transplantation

2009 ◽  
Vol 56 (S 01) ◽  
Author(s):  
N Reiss ◽  
U Schütt ◽  
G Kleikamp ◽  
R Körfer
Keyword(s):  
Heart Transplantation ◽  
Surgical Therapy ◽  
Ebstein’S Anomaly ◽  
Valve Repair ◽  
Ebstein's Anomaly

scholarly journals Ebstein’s Anomaly Corrected by Tissue Valve: Case Report

1970 ◽  
Vol 1 (1) ◽  
pp. 112-114
Author(s):  
SAMA Sabur ◽  
Z Rashid ◽  
A Fazel ◽  
MMG Chowdhury ◽  
M Zaman ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Congenital Heart ◽  
Heart Diseases ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly ◽  
Wpw Syndrome ◽  
Tissue Valve ◽  
Bidirectional Glenn Shunt

Ebstein’s anomaly is a rare form of congenital heart disease with incidence of 1% of all congenital heart diseases. There are two modes of surgical correction of Ebstein’s anomaly: either biventricular repair with or without tricuspid valve replacement, or palliative univentricular repair consisting of bidirectional Glenn shunt or Fontan procedure. We treated a case of severe form of Ebstein’s anomaly with ASD secundum with WPW syndrome. Radiofrequency ablation was done to treat WPW syndrome preoperatively. Celermajer’s index is a prognostic indicator for tricuspid valve repair or replacement. On 04.03.08 tricuspid valve was replaced with 31 mm Carpentier-Edwards bovine pericardial valve under cardiopulmonary bypass. Postoperative period was uneventful. Follow up echo done on 01.06.08 which revealed normally functioning tissue valve found in tricuspid position TR Grade I. So, in conclusion, preoperative evaluation and workout of Celermajer’s index is essential before surgical intervention for decision of tricuspid valve repair or replacement. Last but not the least, any event of arrhythmia should be properly evaluated.Key words: Ebstein’s anomaly, WPW (Wolff- Parkinson-White) Syndrome, Celermajer’s index, Tissue valve. DOI: http://dx.doi.org/10.3329/cardio.v1i1.8213 Cardiovasc. j. 2008; 1(1) : 112-114  

A case of redo tricuspid valve repair after neonatal cone operation for Ebstein’s anomaly

2021 ◽  
Author(s):  
Junya Nabeshima ◽  
Masaaki Yamagishi ◽  
Yoshinobu Maeda ◽  
Hisayuki Hongu ◽  
Hiroki Nakatsuji ◽  
...  
Keyword(s):  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly

Tricuspid Valve Repair for Ebstein’s Anomaly in Young Children: A 30-Year Experience

2006 ◽  
Vol 81 (2) ◽  
pp. 690-696 ◽  
Author(s):  
Umar S. Boston ◽  
Joseph A. Dearani ◽  
Patrick W. O’Leary ◽  
David J. Driscoll ◽  
Gordon K. Danielson
Keyword(s):  
Young Children ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly

Posterior annular plication: tricuspid valve repair in Ebstein's anomaly

2004 ◽  
Vol 77 (6) ◽  
pp. 2167-2171 ◽  
Author(s):  
Camille L Hancock Friesen ◽  
Robert Chen ◽  
Jonathan G Howlett ◽  
David B Ross
Keyword(s):  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Repair ◽  
Ebstein's Anomaly

Modified Starnes procedure as a bridge to 2-ventricle repair in neonatal Ebstein’s anomaly: A paradigm shift

2021 ◽  
Keyword(s):  
Tricuspid Valve ◽  
Single Ventricle ◽  
Hemodynamic Instability ◽  
Ebstein’S Anomaly ◽  
Tricuspid Valve Repair ◽  
Valve Regurgitation ◽  
Valve Repair ◽  
Tricuspid Valve Regurgitation ◽  
Ebstein's Anomaly ◽  
Single Ventricle Palliation

Severe tricuspid valve regurgitation secondary to Ebstein’s anomaly represents several challenges in neonates. It can result in significant respiratory and/or hemodynamic compromise that mandates urgent interventions. When conservative management fails, 2 surgical options are available: tricuspid valve repair or single ventricle palliation. The overall results of neonatal tricuspid valve repair are unsatisfactory especially in sick neonates and those with preoperative hemodynamic instability. Single ventricle palliation utilizing the Starnes procedure with right ventricular exclusion provides a quicker way to improve hemodynamics and allows rapid decompression of the right ventricle but carries the long-term disadvantages of the single ventricle pathway. We were recently faced with a challenging case of neonatal Ebstein’s anomaly resulting in severe tricuspid valve regurgitation (TR) and significant hemodynamic and respiratory instability. We performed an initial stage I palliation with a modified Starnes’ procedure, which allowed stabilization and rapid recovery of the patient to be followed 5 months later with conversion to 2-ventricle repair using the cone technique. We believe combining these 2 strategies for suitable neonatal candidates may be a useful technique that should be considered in the algorithm for neonatal Ebstein’s anomaly.

Successful Bridge to Heart Transplantation in a Patient with Ebstein's Anomaly

1997 ◽  
Vol 5 (4) ◽  
pp. 239-240
Author(s):  
Mitsuhiro Hachida ◽  
Kazutomo Minami ◽  
Michael Koerner ◽  
Michael Morshuis ◽  
Heinrich Koertke ◽  
...  
Keyword(s):  
Cardiopulmonary Bypass ◽  
Heart Transplantation ◽  
Atrial Septal Defect ◽  
Septal Defect ◽  
Left Ventricular ◽  
Ebstein’S Anomaly ◽  
Mechanical Support ◽  
Tricuspid Valve Replacement ◽  
Ventricular Failure ◽  
Ebstein's Anomaly

A 52-year-old female was diagnosed with Ebstein's anomaly and an associated atrial septal defect. She underwent closure of the atrial septal defect and tricuspid valve replacement. Severe left ventricular failure was found after discontinuation of cardiopulmonary bypass, thus biventricular mechanical support was established. Four days later the patient underwent successful heart transplantation and was discharged without any complications.

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