scholarly journals Adrenocortical sarcomatoid carcinoma: a case report and review of the literature

2020 ◽  
Vol 2020 (7) ◽  
Author(s):  
Derqaoui Sabrine ◽  
Bernoussi Zakia ◽  
Znati Kaoutar
Keyword(s):  
Poor Prognosis ◽  
Sarcomatoid Carcinoma ◽  
Rare Entity ◽  
Rare Cancer ◽  
Review Of The Literature ◽  
Epithelioid Cells ◽  
Poorly Differentiated Carcinoma ◽  
S 100 ◽  
Poorly Differentiated ◽  
The Right

Abstract Adrenal sarcomatoid carcinoma (ASC) is a very rare aggressive variant of adrenocortical carcinoma showing carcinomatous and sarcomatous differentiation. It is a poorly differentiated carcinoma with poor prognosis. The diagnosis requires careful histological and immunohistochemical investigation. We describe a new case of ASC to raise awareness on this extremely rare entity. A 27-year-old woman presented with a right flank pain. Imaging revealed a tissular mass of the right adrenal gland without metastases. After adrenalectomy, histology revealed sheets of epithelioid cells that stained for synaptophysin and Melan-A; and spindled cells staining for S-100. We have reported the clinical and histopathological features of ACS’s case; as it is an extremely rare cancer with a challenging diagnosis. There is a need for a further understanding of ASC’s biology to improve it poor prognosis.

scholarly journals Squamous Cell Carcinoma of Kidney and Its Prognosis: A Case Report and Review of the Literature

2015 ◽  
Vol 2015 ◽  
pp. 1-3 ◽  
Author(s):  
Tapan Kumar Sahoo ◽  
Saroj Kumar Das ◽  
Chandraprava Mishra ◽  
Ipsita Dhal ◽  
Rohani Nayak ◽  
...  
Keyword(s):  
Squamous Cell Carcinoma ◽  
Cell Carcinoma ◽  
Squamous Cell ◽  
Radical Nephrectomy ◽  
Advanced Stage ◽  
Rare Entity ◽  
Primary Squamous Cell Carcinoma ◽  
Review Of The Literature ◽  
Radiological Features ◽  
The Right

Primary squamous cell carcinoma of the renal parenchyma is an extremely rare entity. The diagnosis of squamous cell carcinoma of the renal pelvis is usually unsuspected due to the rarity and inconclusive clinical and radiological features. Most of the patients are diagnosed at an advanced stage and are with poor outcome. Radical nephrectomy is the mainstay of the treatment. We reported a case of squamous cell carcinoma of the kidney in a 50-year-old female who presented with the right sided abdomen pain. The patient was treated with radical nephrectomy.

METASTASIS OF AN ADENOCARCINOMA OF THE STOMACH TO THE 4TH METACARPAL BONE

Hand Surgery ◽  
2001 ◽  
Vol 06 (02) ◽  
pp. 239-242 ◽  
Author(s):  
H. C. Chang ◽  
K. H. Lew ◽  
C. O. Low
Keyword(s):  
Metastatic Lesion ◽  
Metacarpal Bone ◽  
Review Of The Literature ◽  
Poorly Differentiated Adenocarcinoma ◽  
Poorly Differentiated ◽  
The Right

Metastatic tumours of the hand are uncommon. The majority of these tumours affect the phalanges and the primary tumours are usually bronchogenic in origin, with breast and kidney tumours next in frequency. Metastatic gastrointestinal to the hand is rare and usually from the colon. We report a case of poorly differentiated adenocarcinoma of the stomach antrum presenting with a metastatic lesion to the right 4th metacarpal bone. A review of the literature is included.

scholarly journals Unique case of inverted papilloma of septum with nasopharyngeal carcinoma: Is it a metachronous tumour?

2020 ◽  
Vol 8 ◽  
pp. 2050313X2092203
Author(s):  
Susanne Flach ◽  
Aaron SJ Ferguson ◽  
Sharon White ◽  
Paul S White ◽  
Jaiganesh Manickavasagam
Keyword(s):  
Malignant Transformation ◽  
Inverted Papilloma ◽  
High Rate ◽  
Unique Case ◽  
Solitary Lesion ◽  
Poorly Differentiated Carcinoma ◽  
Nasopharyngeal Biopsy ◽  
Poorly Differentiated ◽  
The Right

Inverted papilloma is a rare and benign tumour. It affects the nasal cavity and paranasal sinuses, has a high rate of recurrence and is associated with malignant transformation. Only few cases of a poorly differentiated carcinoma arising from inverted papilloma have been reported, none of which in the nasopharynx. We report a case of a 37-year-old female, who presented originally in 2012 with inverted papilloma of the nasal septum which was surgically resected. Nasopharyngeal biopsy from 2014 was reported as carcinoma in situ and treated with local endoscopic resection. Three years later she presented with a solitary lesion of the right Eustachian tube opening, confirmed as invasive poorly differentiated carcinoma. Imaging revealed T4 N2b M0 malignancy with skull base and prevertebral space invasion, likely extension into right temporal lobe and malignant adenopathy. Although rare, malignant transformation of inverted papilloma in unusual places should be considered during workup and monitoring of patients.

scholarly journals Metastasizing Malignant Granular Cell Tumor (Abrikossoff Tumor) of the Anterior Abdominal Wall, with Prolonged Survival

2019 ◽  
Vol 2019 ◽  
pp. 1-8
Author(s):  
Yara A. Alnashwan ◽  
Khaled A. H. Ali ◽  
Samir S. Amr
Keyword(s):  
Abdominal Wall ◽  
Poor Prognosis ◽  
Granular Cell Tumor ◽  
Anterior Abdominal Wall ◽  
Granular Cell ◽  
Cell Tumor ◽  
Prolonged Survival ◽  
Review Of The Literature ◽  
Malignant Granular Cell Tumor ◽  
The Right

Malignant granular cell tumor (MGCT) is a rare high-grade mesenchymal tumor of Schwann cell origin. MGCTs commonly affect thigh, extremity, and trunk; however, involvement of the abdominal wall is quite rare. It has poor prognosis with 39% mortality rate in 3-year interval. We report a 50-year-old female who had MGCT arising in the anterior abdominal wall and developed massive metastatic deposits in both lungs and in the right inguinal lymph nodes, with prolonged survival for 11 years. A brief review of the literature is presented.

Angioma Serpiginosum with Linear Distribution: Case Report and Review of the Literature

2008 ◽  
Vol 12 (4) ◽  
pp. 180-183 ◽  
Author(s):  
Mike S. Kalisiak ◽  
Richard M. Haber
Keyword(s):  
Case Report ◽  
Vascular Anomaly ◽  
Rare Entity ◽  
Review Of The Literature ◽  
Linear Distribution ◽  
Delayed Treatment ◽  
Skin Biopsies ◽  
The Common ◽  
The Right ◽  
Histopathologic Findings

Background: Angioma serpiginosum is a vascular anomaly that classically presents in childhood and predominantly affects females. Objective: To present a case of a young woman with linear distribution of angioma serpiginosum and review the common clinical characteristics and presentation of this condition. Methods: Case report with skin biopsies and dermoscopic findings. Results: A clinical examination revealed numerous irregular punctate red macules in a linear distribution over the right arm. On dermoscopy, the lesions appeared as multiple sharply demarcated red lagoons. The histopathologic findings of dilated blood vessels in the papillary dermis with absence of other changes confirmed the diagnosis of angioma serpiginosum. Conclusion: Angioma serpiginosum is a rare entity that can be distinguished by clinical and histopathologic examinations. Lack of recognition of this condition may lead to unnecessary investigations and delayed treatment.

scholarly journals Ganglioneuromatous Polyposis of the Colon: a Case Report and a Review of the Literature

2011 ◽  
Vol 02 (01) ◽  
pp. 018-021
Author(s):  
Cristina D'Ercole ◽  
Angelo Zullo ◽  
Maria Consiglia Bragazzi ◽  
Cesare Hassan ◽  
Roberto Lorenzetti ◽  
...  
Keyword(s):  
Nervous System ◽  
Abdominal Pain ◽  
Clinical Signs ◽  
Rare Entity ◽  
Ascending Colon ◽  
Review Of The Literature ◽  
Endoscopic Feature ◽  
Systemic Manifestations ◽  
The Right ◽  
Intestinal Ganglioneuromatosis

ABSTRACTThis report discusses a case of ganglioneuromatous polyposis of the colon in a woman without any other systemic manifestations. To our knowledge, this is the first report of the few cases of intestinal ganglioneuromatosis described in the literature presenting with abdominal pain and bloody diarrhea as unique clinical signs, with multiple polyps confined in the right side of the transverse colon and in the ascending colon. Of note, the endoscopic feature of such a rare entity - which involves the enteric nervous system - may mimic that of sessile adenomatous polyps which are diagnosed at routine colonoscopy. We emphasized that this condition may be misdiagnosed, and we reviewed the reported cases in the literature. (J Dig Endosc 2011;2(1):18-21)

Eyelid Phakomatous Choristoma

2003 ◽  
Vol 13 (5) ◽  
pp. 482-485 ◽  
Author(s):  
E. Mencía-Gutiérrez ◽  
E. Gutiérrez-Díaz ◽  
J.R. Ricoy ◽  
B. Sarmiento-Torres
Keyword(s):  
Epithelial Membrane Antigen ◽  
Subcutaneous Tissue ◽  
Periodic Acid ◽  
Lower Eyelid ◽  
Rare Entity ◽  
Periodic Acid Schiff ◽  
S 100 ◽  
The Right ◽  
Intense Immunoreactivity ◽  
Histopathologic Features

Purpose To report a case of congenital phakomatous choristoma (PC) of the eyelid, a rare tumor of lenticular anlage in the subcutaneous tissue and dermis. Case A boy had a mass in the right lower eyelid near the inner canthus at birth. At age 10 months, the tumor was excised. Results The tumor cells showed intense immunoreactivity positive for S-100 protein, vimentin, and periodic acid-Schiff. Keratin markers, epithelial membrane antigen, glial fibrillary acidic protein, muscle specific actin, and epithelial membrane antigen were negative. The histopathologic features were consistent with those of a PC. Conclusions This histopathologic and immunoreactivity study supports the proposal that PC is a rare entity of lenticular anlage origin. Only 18 such cases have been described previously.

scholarly journals Sarcomatous Carcinoma of the Orbit: A Case Report and Review of the Literature

2015 ◽  
Vol 6 (2) ◽  
pp. 180-185
Author(s):  
Ninan Mathew ◽  
Mathen Mathew ◽  
Jon Farrah
Keyword(s):  
Case Report ◽  
Poor Prognosis ◽  
Advanced Disease ◽  
English Literature ◽  
Treatment Options ◽  
Malignant Cells ◽  
Review Of The Literature ◽  
Immunological Markers ◽  
Rare Tumours ◽  
The Right

Sarcomatous carcinomas (SCs) are rare tumours that contain malignant cells with epithelial and mesenchymal characteristics. SC rarely presents in the head and neck, and occurs even less often in the orbit. Only 8 cases of SCs located in the orbit or affecting the globe function have been described in the English literature. Here, we report a case of SC affecting the right orbit. SC is associated with a poor prognosis and advanced disease at presentation. Diagnosis is difficult, as histology often fails to definitively identify SC, necessitating a wide panel of molecular/immunological markers. Treatment options are generally aggressive but risky, and frequently yield poor results. Due to the rarity of SC, there has been little focus on the development of improved treatment options.

scholarly journals Recurrent Primary Intrasellar Paraganglioma

2020 ◽  
Vol 2020 ◽  
pp. 1-6
Author(s):  
Elizabeth A. Schueth ◽  
Daniel C. Martinez ◽  
Charles G. Kulwin ◽  
Jose M. Bonnin ◽  
Troy D. Payner ◽  
...  
Keyword(s):  
Sella Turcica ◽  
Visual Field Defects ◽  
Rare Entity ◽  
Immunohistochemical Examination ◽  
Surgical Interventions ◽  
Suprasellar Region ◽  
S 100 ◽  
Blurry Vision ◽  
Aggressive Tumor ◽  
The Right

We describe a case of an 81-year-old male presenting with bitemporal visual field defects and blurry vision in the right eye. The patient was found to have a recurrent primary paraganglioma in the sellar and suprasellar region requiring a repeat transsphenoidal endoscopic resection. Immunohistochemical examination confirmed paraganglioma with the classic zellballen appearance which stained positive for chromogranin, synaptophysin, and S-100 in the periphery. Paragangliomas (PGLs) in the sella turcica are a rare entity; only 19 cases have ever been reported in the literature. PGLs in the sellar region are often misdiagnosed or diagnosed in a delayed fashion. Earlier diagnosis of this locally aggressive tumor and meticulous debulking can prevent morbidity secondary to the tumor’s compressive effects. This report highlights the effectiveness of surgical interventions in treatment of paragangliomas. More research is still needed to determine the need for adjuvant therapies such as radiation.

scholarly journals Transoral Laser Surgery for Adenosquamous Carcinoma of the Glottis: First Case Report and Review of the Literature

2020 ◽  
pp. 014556132091657
Author(s):  
William Kendall ◽  
Panagiotis A. Dimitriadis ◽  
Fawzia Tahir ◽  
Sara Sionis
Keyword(s):  
Squamous Cell Carcinoma ◽  
Case Report ◽  
Laser Surgery ◽  
Poor Prognosis ◽  
Adenosquamous Carcinoma ◽  
Severe Dysplasia ◽  
Rare Cancer ◽  
Review Of The Literature ◽  
First Case ◽  
Disease Free

Adenosquamous carcinoma of the head and neck is a rare cancer associated with poor prognosis. Histologically, it is identified through the presence of both adenocarcinoma and squamous cell carcinoma, although it may be difficult to diagnose from initial endoscopic biopsies. We report a case of adenosquamous carcinoma of the glottis in an 82-year-old female patient who presented with progressive hoarseness of voice and in whom initial biopsies had shown only moderate to severe dysplasia. This is the first case in the literature of a primary adenosquamous carcinoma of the glottis managed successfully with a CO2 laser left type Va cordectomy. The patient remained disease-free 28 months postoperatively.

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