Parapharyngeal Ganglioneuroma with Neurofibromatosis: An Unusual Presentation

2011 ◽  
Vol 120 (12) ◽  
pp. 769-774 ◽  
Author(s):  
Parul Sinha ◽  
Suresh C. Sharma ◽  
Shipra Agarwal ◽  
Siddhartha Datta Gupta
Keyword(s):  
Unusual Case ◽  
Benign Tumor ◽  
Parapharyngeal Space ◽  
Treatment Approach ◽  
Hypertensive Crisis ◽  
Neurogenic Tumors ◽  
Appropriate Treatment ◽  
Rare Benign Tumor ◽  
Hypertensive Crises ◽  
Biochemical Features

Objectives: Ganglioneuroma is a rare benign tumor of the sympathetic nervous system that is seldom localized to the head and neck. Rarer still are cases of functional ganglioneuroma with catecholamine production. We report an unusual case of a large parapharyngeal space ganglioneuroma in a patient with neurofibromatosis that caused an intraoperative hypertensive crisis in the absence of a neuroblastomatous component — Hitherto an undocumented complication. Methods: We present a case of functional parapharyngeal ganglioneuroma and review the clinicopathologic and biochemical features of these rare tumors. Results: Fewer than 40 anecdotal cases of parapharyngeal ganglioneuromas have been reported, and there is a lack of ade quate literature on the biology and appropriate treatment approach of these tumors. Conclusions: Our case illustrates the importance of vigilant preoperative precautions in the management of neurogenic tumors, particularly ganglioneuromas. These usually nonfunctional tumors can result in sudden intraoperative and postoperative hypertensive crises even in the absence of any preoperative autonomic symptoms.

scholarly journals Prenatal Diagnosis of Congenital Mesenchymal Hamartoma of Liver: A Case Report

2011 ◽  
Vol 2011 ◽  
pp. 1-3 ◽  
Author(s):  
Sreelakshmi Kodandapani ◽  
Muralidhar V. Pai ◽  
Vijay Kumar ◽  
Kanthilatha V. Pai
Keyword(s):  
Case Report ◽  
Prenatal Diagnosis ◽  
Unusual Case ◽  
Benign Tumor ◽  
Mesenchymal Hamartoma ◽  
Rare Benign Tumor ◽  
Abdominal Cyst

Hepatic mesenchymal hamartoma is a rare benign tumor. We present an unusual case of a fetal abdominal cyst, later diagnosed histopathologically to be mesenchymal hamartoma of liver. The organ of origin was indeterminate on both prenatal and postnatal ultrasounds. As there are no specific sonological findings, whenever a large multicystic fetal abdominal cyst is seen, mesenchymal hamartoma should be considered as a possibility.

scholarly journals Rhabdomyoma of the parapharyngeal space

2021 ◽  
Vol 106 (106(813)) ◽  
pp. 215-217
Author(s):  
C. Acosta-Vásquez ◽  
L. Uceda-Carrascosa ◽  
F. Leiva-Cepas ◽  
L. Rodríguez-Pérez
Keyword(s):  
Head And Neck ◽  
Clinical Case ◽  
Benign Tumor ◽  
Parapharyngeal Space ◽  
Asymptomatic Patient ◽  
Histological Study ◽  
Mesenchymal Tumor ◽  
Skeletal Tissue ◽  
Rare Benign Tumor ◽  
Ct And Mri

Rhabdomyoma is a benign tumor that comes from skeletal tissue, it is classified as cardiac and extracardiac according to the location. Extracardiac rhabdomyomas most frequently originate in the head and neck at the larynx and pharynx, being the parapharyngeal space an exceptional location. We present the clinical case of an 86-year-old man asymptomatic patient with a laterocervical mass with years of evolution, that has increased its size progressively, with dysphagia and dyspnea on exertion in the last years. CT and MRI were requested, which provided dimensions, location at the parapharyngeal space, as well as signs of benignity. The FNA results indicated that it was a mesenchymal tumor. After cervicotomy and histological study, the diagnosis of parapharyngeal space rhabdomyoma was confirmed. We conducted a bibliographic review of this extremely rare benign tumor at the head and neck level.

scholarly journals First Report of a Lipoblastoma of the Parapharyngeal Space

2002 ◽  
Vol 81 (8) ◽  
pp. 564-568 ◽  
Author(s):  
Kalpana DePasquale ◽  
Daniel G. Deschler
Keyword(s):  
Differential Diagnosis ◽  
Head And Neck ◽  
Benign Tumor ◽  
Parapharyngeal Space ◽  
First Report ◽  
Parotid Region ◽  
Rare Benign Tumor ◽  
A Site

Lipoblastoma is a rare benign tumor that occurs primarily in children younger than 3 years of age. Fewer than 100 cases have been reported in the literature, and only eight cases have been previously reported in the head and neck; two of them occurred in the parotid region, where the differential diagnosis becomes quite extensive. We report a new case of head and neck lipoblastoma—one that occurred in the parapharyngeal space, a site that has not been previously reported. By doing so, we hope to promote awareness and consideration of lipoblastoma in the differential diagnosis of deep-parotid and para-pharyngeal-space neoplasms.

scholarly journals Giant Adrenal Lipoma with Hemorrhage Requiring Extended Surgical Resection

2021 ◽  
pp. 978-984
Author(s):  
Kanji Otsubo ◽  
Shinjiro Kobayashi ◽  
Keisuke Ida ◽  
Masafumi Katayama ◽  
Satoshi Koizumi ◽  
...  
Keyword(s):  
Surgical Resection ◽  
Benign Tumor ◽  
Case Reports ◽  
Treatment Algorithm ◽  
Surrounding Tissue ◽  
Adrenal Tumors ◽  
Active Hemorrhage ◽  
Appropriate Treatment ◽  
Histopathologic Diagnosis ◽  
Rare Benign Tumor

Adrenal lipoma is a rare, benign tumor, reported to account for 0.7% of primary adrenal tumors. A 69-year-old man presented with left lateral abdominal pain. Computed tomography (CT) was performed, and a huge, irregularly shaped retroperitoneal tumor of uneven internal density was identified, with the border between the tumor and the pancreas and kidney being unclear. Active hemorrhage was also depicted. The tumor consisted mainly of fat, with the exception of the hematoma; it measured 200 mm; and the boundary between it and nearby organs, such as the pancreas, was unclear. Despite angiography being performed twice, the responsible vessel was not identified. Thus, for the purpose of both diagnosis and treatment, we resected the tumor, and considering the possibility of a malignancy, such as liposarcoma, we also resected the pancreatic body and tail and the spleen. The final histopathologic diagnosis was benign adrenal lipoma with hemorrhage, with no invasion to surrounding tissue. Hemorrhage within an adrenal tumor is rare. Most adrenal lipomas are small “incidentalomas” and asymptomatic. With development of a large adrenal lipoma comes the possibility of hemorrhage along with the possibility of features suggestive of malignancy. We encountered a giant adrenal lipoma with hemorrhage and, because of the aforementioned features, performed extended surgical resection, seen in retrospect as oversurgery. The widespread use of CT has led to an increased number of reported cases of adrenal lipoma. We anticipate an accumulation of case reports, which will allow for development of an appropriate treatment algorithm.

scholarly journals Dentofacial Deformity Caused by Bulky Osteochondroma: Report of an Unusual Case and the Importance of Cone Beam Computed Tomography

2017 ◽  
Vol 11 (1) ◽  
pp. 237-241 ◽  
Author(s):  
Weeraya Tantanapornkul ◽  
Kittipong Dhanuthai ◽  
Phonkit Sinpitaksakul ◽  
Chumpot Itthichaisri ◽  
Paksinee Kamolratanakul ◽  
...  
Keyword(s):  
Computed Tomography ◽  
Differential Diagnosis ◽  
Case Report ◽  
Unusual Case ◽  
Benign Tumor ◽  
Mandibular Condyle ◽  
Cone Beam ◽  
Dentofacial Deformity ◽  
Alternative Modality ◽  
Rare Benign Tumor

Introduction: Osteochondroma of mandibular condyle is a rare benign tumor. Case Report: This case report described clinical, radiographic features, differential diagnosis, histopathologic correlation and treatment of condylar osteochondroma. Conclusion: Conebeam computed tomography (CBCT) is an alternative modality to CT or MRI that should be performed in all cases of suspected osteochondroma of the mandibular condyle.

Ancient Schwannoma of the Submandibular Gland: A Case Report

1996 ◽  
Vol 75 (12) ◽  
pp. 781-783 ◽  
Author(s):  
Peter C. Bondy ◽  
Robert M. Block ◽  
Jimmy Green
Keyword(s):  
Case Report ◽  
Submandibular Gland ◽  
Unusual Case ◽  
Benign Tumor ◽  
Rare Entity ◽  
Neurogenic Tumors ◽  
Malignant Mesenchymal Tumor ◽  
Surgical Aspects ◽  
Slow Growing ◽  
Neural Sheath

Schwannomas (neurilemmomas) are neurogenic tumors that arise from the Schwann cells of the neural sheath. They are most often benign and solitary. Extracranial schwannomas are rare, and can be mistaken for metastatic disease or other non-neurogenie tumors. Ancient schwannoma is a rare variant of schwannoma with a course typical of a slow-growing benign tumor. Histologically, it can be confused with a malignant mesenchymal tumor. An unusual case of an ancient schwannoma of the submandibular gland is reported. The clinical, histological and surgical aspects of this tumor are discussed, and the literature regarding this rare entity is reviewed.

An Invasive Hemolymphangioma of the Pancreas in a Young Woman

2019 ◽  
Vol 21 (10) ◽  
pp. 798-800 ◽  
Author(s):  
Zhijun Zhang ◽  
Qinghong Ke ◽  
Weiliang Xia ◽  
Xiuming Zhang ◽  
Yan Shen ◽  
...  
Keyword(s):  
Computed Tomography ◽  
Case Report ◽  
Young Woman ◽  
Benign Tumor ◽  
Abdominal Distension ◽  
Accurate Diagnosis ◽  
Cystic Tumor ◽  
Rare Benign Tumor ◽  
Radical Surgical Resection

Background: Hemolymphangioma is a rare benign tumor. To the best of our knowledge, there were only 10 reports of this tumor of the pancreas until March 2018. Case Report: Here, we reported a large invasive hemolymphangioma of the pancreas in a young woman with a complaint of abdominal distension and an epigastric mass about 3 weeks. She was found to have a huge multilocular cystic tumor at the neck and body of pancreas on computed tomography. She was eventually diagnosed with hemolymphangioma of the pancreas after operation. After 2 years of follow-up, there was no signs of recurrence. Conclusion: From our case and literature, we can conclude that hemolymphangioma of the pancreas is uncommon benign tumor, and it is hard to make an accurate diagnosis preoperatively. Radical surgical resection should be performed whenever possible. The prognosis of this disease seems good.

Testicular fibroma: A case report

2013 ◽  
Vol 21 (3-4) ◽  
pp. 139-140
Author(s):  
Sunita Shere ◽  
Anjali Kulkarni ◽  
Shubhjyoti Pore ◽  
Rajan Bindu
Keyword(s):  
Case Report ◽  
Benign Tumor ◽  
Histopathological Diagnosis ◽  
Testicular Mass ◽  
Rare Benign Tumor ◽  
Testicular Malignancy ◽  
Slow Growing

Testicular fibroma of gonadal stromal origin is a rare benign tumor of testis, which usually presents as a slow growing testicular mass. Intratesticular fibroma of gonadal stromal origin, with or without minor sex cord elements, must be considered, analogous to similar tumors in ovary, as a benign tumor. Until now, only 25 cases of testicular fibroma have been reported in the literature. We reported a case of testicular fibroma in a 20 years male who presented with painless right testicular enlargement since two years. Ultrasonography (USG) showed heterogeneous mass in right scrotum suggestive of testicular malignancy. Right orchidectomy was done. Histopathological diagnosis was testicular fibroma, which was confirmed by immunohistochemistry.

scholarly journals Management of Basal Cell Adenoma of Accessory Parotid Gland Through Transoral Approach: Report of a Rare Case With Review

2021 ◽  
Vol 6 ◽  
pp. 247275122110308
Author(s):  
Charudatta Naik ◽  
Sanjay Joshi ◽  
Bhupendra Mhatre ◽  
Sneha Punamiya
Keyword(s):  
Parotid Gland ◽  
Basal Cell ◽  
Benign Tumor ◽  
Transoral Approach ◽  
Surgical Approaches ◽  
Basal Cell Adenoma ◽  
Diagnostic Dilemma ◽  
Cell Adenoma ◽  
Rare Benign Tumor ◽  
Accessory Parotid Gland

Diagnosis of mid-cheek mass has always been a diagnostic dilemma for clinicians. The incidence of the accessory parotid gland (APG) has been well documented in the literature. However, a diverse spectrum of pathologies can arise from this accessory parotid tissue. Basal cell adenoma is a rare benign tumor that predominantly affects the parotid gland. Its occurrence in the accessory parotid gland has been documented in 9 cases till date. Surgical approaches for the management of such APG lesions have been in debate. This report documents a case of Basal Cell Adenoma arising in accessory parotid tissue in a 55-year-old woman who was treated by transoral excision. This paper also reviews previously documented cases of all APG lesions and attempts to elucidate the rationale for selecting an appropriate surgical approach.

Robotic, totally endoscopic excision of mitral valve papillary fibroelastoma

2021 ◽  
Keyword(s):  
Mitral Valve ◽  
Aortic Valve ◽  
Tricuspid Valve ◽  
Benign Tumor ◽  
Pulmonary Valve ◽  
Papillary Fibroelastoma ◽  
Robotic Assisted ◽  
Endoscopic Excision ◽  
Rare Benign Tumor ◽  
Sixth Decade

Papillary fibroelastoma is a rare, benign tumor that affects males more frequently than females and that tends to be diagnosed during the fifth or sixth decade of life. It tends to arise on cardiac valves, with the aortic valve being the most frequent location followed by the mitral valve, the tricuspid valve, and the pulmonary valve. We present the case of a robotic-assisted, totally endoscopic excision of a mitral valve papillary fibroelastoma.

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