scholarly journals PKD1-associated autosomal dominant polycystic kidney disease with glomerular cysts presenting with nephrotic syndrome caused by focal segmental glomerulosclerosis

2019 ◽  
Vol 20 (1) ◽  
Author(s):  
Yasuhiro Oda ◽  
Naoki Sawa ◽  
Eiko Hasegawa ◽  
Hiroki Mizuno ◽  
Masahiro Kawada ◽  
...  
Keyword(s):  
Nephrotic Syndrome ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Focal Segmental Glomerulosclerosis ◽  
Autosomal Dominant ◽  
Polycystic Kidney ◽  
Segmental Glomerulosclerosis ◽  
Glomerular Cysts ◽  
Autosomal Dominant Polycystic Kidney

Nephrotic Syndrome and Rapid Renal Failure in Autosomal Dominant Polycystic Kidney Disease

1990 ◽  
Vol 10 (1) ◽  
pp. 69-72 ◽  
Author(s):  
Gayle Murphy ◽  
Antonios H. Tzamaloukas ◽  
Margaret B. Listrom ◽  
Lawrence J. Gibel ◽  
Suzanne Meleg Smith ◽  
...  
Keyword(s):  
Renal Failure ◽  
Nephrotic Syndrome ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Autosomal Dominant ◽  
Polycystic Kidney ◽  
Autosomal Dominant Polycystic Kidney

scholarly journals Nephrotic syndrome and autosomal dominant polycystic kidney disease

2012 ◽  
Vol 5 (6) ◽  
pp. 508-511 ◽  
Author(s):  
B. Visciano ◽  
R. A. Di Pietro ◽  
R. Rossano ◽  
A. Mancini ◽  
P. Zamboli ◽  
...  
Keyword(s):  
Nephrotic Syndrome ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Autosomal Dominant ◽  
Polycystic Kidney ◽  
Autosomal Dominant Polycystic Kidney

scholarly journals Nephrotic syndrome in autosomal dominant polycystic kidney disease.

1995 ◽  
Vol 6 (5) ◽  
pp. 1354-1359
Author(s):  
G Contreras ◽  
A Mercado ◽  
V Pardo ◽  
C A Vaamonde
Keyword(s):  
Nephrotic Syndrome ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Minimal Change Disease ◽  
Autosomal Dominant ◽  
Polycystic Kidney ◽  
Protein Excretion ◽  
Histopathologic Evaluation ◽  
Autosomal Dominant Polycystic Kidney ◽  
Nephrotic Range Proteinuria

Urinary protein excretion is generally less than 1 g/24 h in autosomal dominant polycystic kidney disease (ADPKD), and the association of the nephrotic syndrome with this condition is considered rare. A patient with ADPKD associated with nephrotic-range proteinuria is described. She exhibited a relatively rapid impairment of her renal function. An open renal biopsy revealed focal segmental glomerulosclerosis (FGS) with features consistent with secondary FGS. Twenty-one patients with ADPKD and nephrotic syndrome were retrieved from the literature. Fourteen of them (including this case) had a histopathologic evaluation, and FGS was the dominant diagnoses (five patients). Next in frequency were minimal-change disease and membranous nephropathy, with two patients each. Five other patients had a variety of diagnoses. Thus, it is difficult to ascertain if these associations are coincidental or represent a specific pathogenetic relationship. The evaluation of the data also suggests that the presence of proteinuria and nephrotic syndrome accelerates the course of ADPKD toward ESRD.

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