scholarly journals Macroglossia and Beckwith-Wiedemann syndrome

2011 ◽  
Vol 139 (5-6) ◽  
pp. 366-369 ◽  
Author(s):  
Dragan Krasic ◽  
Predrag Radovic ◽  
Nikola Buric ◽  
Dragana Krasic ◽  
Zoran Pesic ◽  
...  
Keyword(s):  
Abdominal Wall ◽  
Leydig Cell ◽  
Umbilical Hernia ◽  
Anterior Abdominal Wall ◽  
Good Condition ◽  
Clinical Signs ◽  
Muscular Hypotonia ◽  
Cell Hyperplasia ◽  
Clinical Criteria ◽  
Swallowing Difficulties

Introduction. In 1963 Beckwith presented a report on the first patient with extreme cytomegaly of adrenal cortex, hyperplasia of kidneys and pancreas and Leydig cell hyperplasia. Wiedemann completed description of the new syndrome by adding umbilical hernia and macroglossia. The diagnosis is made based on the clinical signs of omphalocele or some other umbilical deformity, macroglossia, congenital asymmetry, visceromegaly (liver, pancreas, and kidneys). Case Outline. A 16-month-old male child was admitted for examination because of macroglossia. He underwent examination on several occasions by an endocrinologist due to recurrent hypoglycaemic crisis. The patient was observed by a paediatric neurophysicatrist for disorders of mental development. Hypoglycaemia, muscular hypotonia of the anterior abdominal wall with umbilical hernia and macroglossia were observed by clinical examination. Inratraoral examination revealed macroglossia with microstomia, suckling and swallowing difficulties, hypotonia of the perioral muscles with increased salivation. It was therefore decided to perform surgical reduction of the prominent tongue and develop good condition for nutrition, speech function and the development of orofacial system. Conclusion. The diagnosis of macroglossia is based on subjective clinical criteria such as the morphology and amount of protrusion of the tongue, difficulty in articulating sounds, breathing, and hypersalivation. Some authors have suggested that the tongue size may be analyzed radiographically with a cephalogram. Treatment of macroglossia is controversial because of the absence of objective clinical criteria.

Anterior abdominal wall necrotizing fasciitis due to strangulated umbilical hernia: a diagnostic dilemma

Grand Rounds ◽  
2013 ◽  
Vol 13 (1) ◽  
pp. 69-73 ◽  
Author(s):  
Michael Bartholomew Mwandri ◽  
Julius Chacha Mwita ◽  
Negussie Alula Bekele ◽  
Ibrahim Mohamed Ali ◽  
Michael Stephen Walsh
Keyword(s):  
Necrotizing Fasciitis ◽  
Abdominal Wall ◽  
Umbilical Hernia ◽  
Anterior Abdominal Wall ◽  
Diagnostic Dilemma

scholarly journals Electrical function of the abdominal muscles after combined plastic of extensive median hernias in the context of connective tissue dysplasia

2019 ◽  
Vol 12 (3) ◽  
pp. 152-157
Author(s):  
Radu Railianu
Keyword(s):  
Connective Tissue ◽  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Clinical Signs ◽  
Clinical Severity ◽  
Abdominal Muscles ◽  
Abdominal Hernias ◽  
Connective Tissue Dysplasia ◽  
Optimal Rehabilitation ◽  
Relaxing Effect

Relevance. Improving the electrical function of abdominal muscles in patients with extensive median hernias of the anterior abdominal wall can be facilitated by optimizing the choice of methods for combined hernioplasty, taking into account the clinical severity of connective tissue dysplasia among the hernia carriers. Objective. Study the electrical function of abdominal muscles after the methods of combined hernioplasty of extensive median hernias, taking into account the severity of connective tissue dysplasia among the hernia carriers. Results.  The average numbers of electromyogram frequencies of the abdominal muscles of patients with extensive median hernias from the group without clinical signs of connective tissue dysplasia were almost the same after all the applied methods of combined hernioplasty. The predominance of the rectus muscles electric function over the lateral abdominal muscles among the patients of this group was 33,5 %. Electrofunctional rehabilitation of the abdominal muscles of patients in the second group of examinations depended on the method of combined hernioplasty and changed in the event of an increase or decrease in the severity of connective tissue dysplasia.  The recovery of electroactivity of abdominal muscles in the postoperative period in patients from the second group was more significant with an increase in the number of abdominal muscles applied to aponeuroses and vagina of relaxing sections, which contributed to an increase in mobility and contractility of the musculoaponeurotic layers of the anterior abdominal wall. Conclusions. Thus, with an increase in the severity of connective tissue dysplasia in patients with extensive median abdominal hernias, the method of combined hernioplasty with the most pronounced relaxing effect in relation to the anterior abdominal wall promoted optimal rehabilitation of abdominal muscles.

scholarly journals eTep-retromuscular Repair for Ventral Hernia; a Technique Closest to Ideal

2020 ◽  
Vol 19 (3-4) ◽  
pp. 151-155
Author(s):  
Aleksandar Mitevski ◽  
Petar Markov
Keyword(s):  
Abdominal Wall ◽  
Ventral Hernia ◽  
Umbilical Hernia ◽  
Anterior Abdominal Wall ◽  
Abdominal Cavity ◽  
Wound Complications ◽  
Suture Repair ◽  
Complication Rates ◽  
Mesh Placement ◽  
Umbilical Hernia Repair

Introduction. Ventral hernia represents a problem for the surgeon and patients alike. eTEP repair is a technique that is minimally invasive, provides lower overall complication rates, decreased wound complications and the recurrence rates and shortens the length of stay in the hospital. Case. We present a case of a 48 year old patient who was admitted to our hospital for elective treatment of recurrent umbilical hernia. The patient had umbilical hernia repair 4 years ago, suture repair without mesh placement was performed according to the information given by the patient. On inspection there is visible supraumbillical scar, 12 cm in length with hernia bulging under the scar which is partially reducible on pressure. Discussion. The eTEP technique is closest to ideal because the abdominal cavity is not penetrated, is lessening the risk of visceral lesions and trocar site hernias, allows local or regional anesthesia, gives unsurpassed views of inguinal region and hernias and reproduces the technique of Rives-Stoppa. In favor to overcome the limitations deriving from the limited surgical field and restricted port set up, this technique has been modified based on the normal anatomy of the abdominal wall naming it depen­dently of the extension of the dissection and the location of the hernia. Conclusion. The extended-TEP (e-TEP) technique is based on the anatomical principle that the extraperitoneal space can be reached from almost anywhere in the anterior abdominal wall. It provides the most of the benefits for the patients but also requires great surgical skill and understanding of the anatomy of the anterior abdominal wall.

scholarly journals Necrotising Fasciitis of lower anterior abdominal wall post lower segment ceaserian section

2018 ◽  
Vol 5 (11) ◽  
pp. 3760
Author(s):  
Mahmood A. Makhdoomi ◽  
Abdelhamid Haraga ◽  
Moly Joseph ◽  
Yasser Al Habeeb
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Subcutaneous Tissue ◽  
Good Condition ◽  
Necrotising Fasciitis ◽  
Uneventful Recovery ◽  
Lower Segment ◽  
Surgical Teams ◽  
The One ◽  
Secondary Closure

Necrotising fasciitis is a rapidly progressive inflammatory infection of the fascia with secondary necrosis of the subcutaneous tissue. The speed of spread is directly proportional to the thickness of the subcutaneous layer. It moves along the fascial plane. We are presenting a case report of 27 years old Saudi female with status post Lower segment caesarian section of 10 days’ duration presented with bluish discoloration of the lower anterior abdominal wall around the surgical scar with necrotic patches and surrounding induration with foul smelling discharge from the one pocket within this area. She underwent successful simultaneous incision and wide debridement of gross necrotic tissues; together with evacuation of the pus followed by secondary closure. Both general and plastic surgical teams were involved. Patient made uneventful recovery and discharged home in good condition.

Determination of clinical efficiency of deproteinized dialysate from blood of milk-fed calves after endoprosthetics in patients with ventral hernias

2020 ◽  
Vol 28 (3) ◽  
pp. 323-333
Author(s):  
Sergej V. Ivanov ◽  
Ilya S. Ivanov ◽  
Evgenij G. Obyedkov ◽  
Liliya P. Popova
Keyword(s):  
Abdominal Wall ◽  
Inflammatory Reaction ◽  
Inflammatory Process ◽  
Anterior Abdominal Wall ◽  
Dynamic Change ◽  
Main Group ◽  
Control Group ◽  
Surgical Department ◽  
Regeneration Stage

Aim. To study the influence of deproteinized dialysate from blood of milk-fed calves on the type of exudative discharge and dynamics of inflammatory reaction after hernia repair with plastics of the anterior abdominal wall with hernioendoprosthesis of polypropylene. Materials and Methods. The study involved 59 patients being on stationary treatment in the surgical department of Kursk Regional Clinical Hospital. Patients were hospitalized for the herniation of small or medium dimension. The patients were divided to two groups: the main (n=30) and control (n=29) groups. After endoprosthetics, the patients of the control group were given complex conservative treatment. The patients of the main group, besides standard treatment, were administered deproteinized dialysate from blood of milk-fed calves intravenously in drips 10 ml + 200 ml of 0.9% sodium chloride solution within 7 days. For cytological examination and determination of the type of cytograms, the traumatic discharge was collected and analyzed using the method of M.F. Kamaev and M.A. Palthsev. Results. Cytomorphometric examination was conducted on the third, fifth and seventh day after endoprosthetics with the aim of studying dynamic changes. Determination of cell composition and also of its changes characteristic of each studied period, was necessary for obtaining further information characterizing inflammatory process in the region of placement of the endoprosthesis. After endoprosthetics in patients who were administered hemodialysate, the inflammatory reaction was less pronounced than in patients who did not receive the preparation. This was associated with a more dynamic change of stages of the inflammatory process. In patients of the main group who received deproteinized dialysate, regenerative type of inflammation first appeared on the fifth day and made 6.9%; by the seventh day the share of patients with the regenerative type rose to 17.5%, while in the patients of the control group no regeneration stage was observed in both periods. Conclusion. Analysis of the efficiency of influence of hemodialysate on the inflammatory reaction in plastics of the anterior abdominal wall with polypropylene endoprosthesis evidences faster course of all stages of inflammation and reduction of its intensity by 10%.

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