Liver transplantation for intermittent acute porphyria resistant to medical treatment

2021 ◽  
Author(s):  
Cándido Alcázar López ◽  
Gonzalo P. Rodríguez Laiz ◽  
Rosario Sánchez Martínez ◽  
Sonia Pascual Bartolome ◽  
José Manuel Ramia
Keyword(s):  
Liver Transplantation ◽  
Medical Treatment ◽  
Acute Porphyria ◽  
Intermittent Acute Porphyria

scholarly journals Early liver transplantation for severe alcoholic hepatitis not responding to medical treatment: results of the French-Belgian prospective study QuickTrans

2020 ◽  
Vol 73 ◽  
pp. S115-S116
Author(s):  
Alexandre Louvet ◽  
Julien Labreuche ◽  
Christophe Moreno ◽  
Claire Vanlemmens ◽  
Romain Moirand ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Prospective Study ◽  
Medical Treatment ◽  
Alcoholic Hepatitis ◽  
Treatment Results ◽  
Severe Alcoholic Hepatitis

Oxygen toxicity related to exposure to lead.

1985 ◽  
Vol 31 (10) ◽  
pp. 1673-1676 ◽  
Author(s):  
H P Monteiro ◽  
D S Abdalla ◽  
A S Arcuri ◽  
E J Bechara
Keyword(s):  
Superoxide Dismutase ◽  
Glutathione Peroxidase ◽  
Protoporphyrin Ix ◽  
Oxygen Toxicity ◽  
Oxygen Species ◽  
Acute Porphyria ◽  
Dose Response Relationship ◽  
Activated Oxygen ◽  
Exposed Workers ◽  
Intermittent Acute Porphyria

Abstract We evaluated superoxide dismutase (EC 1.15.1.1) and glutathione peroxidase (EC 1.11.1.9) activities in the erythrocytes of lead-exposed and nonexposed workers from distinct industries localized in the State of São Paulo, Brazil. Concentrations of either lead or protoporphyrin IX, or both, in blood were used to indicate the extent of exposure. In all cases, values for superoxide dismutase were significantly higher in the exposed workers. The dose-response relationship between this enzyme and lead concentrations was roughly linear for the workers with greater than 40 micrograms of lead per 100 g of blood. Except for the sample from one of the industries, the corresponding glutathione peroxidase activities were also significantly higher in lead-exposed workers. These data, together with those previously found for patients with intermittent acute porphyria, suggest that in both groups the accumulation of heme precursors is connected to the exacerbated production of activated oxygen species.

Intermittent Acute Porphyria Treated with Chlorpromazine

1957 ◽  
Vol 256 (7) ◽  
pp. 309-311 ◽  
Author(s):  
Robert N. Monaco ◽  
Robert D. Leeper ◽  
Jacob J. Robbins ◽  
George L. Calvy
Keyword(s):  
Acute Porphyria ◽  
Intermittent Acute Porphyria

scholarly journals Decreased Red Cell Uroporphyrinogen I Synthetase Activity in Intermittent Acute Porphyria

1972 ◽  
Vol 51 (10) ◽  
pp. 2530-2536 ◽  
Author(s):  
L. James Strand ◽  
Urs A. Meyer ◽  
Bertram F. Felsher ◽  
Allan G. Redeker ◽  
Harvey S. Marver
Keyword(s):  
Synthetase Activity ◽  
Red Cell ◽  
Acute Porphyria ◽  
Intermittent Acute Porphyria

DETECTION OF INTERMITTENT ACUTE PORPHYRIA TRAIT IN CHILDREN

The Lancet ◽  
1976 ◽  
Vol 308 (7978) ◽  
pp. 201-202 ◽  
Author(s):  
Yves Nordmann ◽  
Bernard Grandchamp ◽  
Mireille Grelier ◽  
N'Guyen Phung ◽  
Hubert De Verneuil
Keyword(s):  
Acute Porphyria ◽  
Intermittent Acute Porphyria
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