A Case of Pulmonary Artery Sarcoma

2020 ◽  
Author(s):  
Yukang Liu ◽  
Yan Hu ◽  
Wei Han ◽  
Jingqun Tang ◽  
Qingchun Liang ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Surgical Resection ◽  
Frozen Section ◽  
Lower Lobe ◽  
Left Pulmonary Artery ◽  
Computed Tomographic Angiography ◽  
Resection Margins ◽  
Pulmonary Artery Sarcoma ◽  
Computed Tomographic ◽  
Isolated Lung

Abstract Background: pulmonary artery sarcoma is a rare mesenchymal tumor. The prognosis of this very infrequent disease remains poor,and surgical resection is important for obtaining the best outcome.Case Presentation: A 51-year-old male patient presented to our clinic due to the finding of the isolated lung mass in the left lower lobe of the lung. Preoperative pulmonary artery computed tomographic angiography scans showed a mass with the in the left pulmonary artery and an isolated mass in the left dorsal segment of the lung (RS6).Under extracorporeal circulation the left pneumonectomy was performed, the surgical resection margins were confirmed to be tumor-free on frozen section and all lymph nodes were free of tumor. Histopathology, immunohistochemistry, as well as fluorescence in situ hybridization(FISH) indicated the diagnosis of pleomorphic rhabdomyosarcomaConclusion: This case report describes a PAS which was successfully resected with pneumonectomy and concludes that biopsy may play a limited role in confirming the pathological type and pneumonectomy should be considered in the surgical treatment of PAS.

Discontinuous Pulmonary Artery

2016 ◽  
Vol 8 (1) ◽  
pp. 106-110 ◽  
Author(s):  
Osama Eltayeb ◽  
Michael C. Mongé ◽  
Andrada R. Popescu ◽  
Anne E. Sarwark ◽  
Tyler Harris ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Arteries ◽  
Left Pulmonary Artery ◽  
Computed Tomographic Angiography ◽  
Computed Tomographic ◽  
Essentially Normal ◽  
Collateral Arteries ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Tomographic Angiography

We describe the diagnosis and surgical repair of a five-month-old infant with a congenital discontinuous right pulmonary artery. Initial echocardiogram failed to show the right pulmonary artery and revealed systemic left pulmonary artery pressure based on the tricuspid regurgitation jet. Computed tomographic angiography confirmed the diagnosis of discontinuous right pulmonary artery. The right pulmonary artery appeared essentially normal in size, and there were no significant aortopulmonary collateral arteries. Using cardiopulmonary bypass and aortic transection, we created an anastomosis between the right and the main pulmonary arteries augmented anteriorly by a pericardial patch. Postoperative lung perfusion scan demonstrated balanced pulmonary blood flow to the lungs. Pulmonary hypertension resolved over three weeks in the postoperative period, an expected outcome in this age-group.

scholarly journals Giant Saphenous Venous Graft Aneurysm with Compression of the Pulmonary Artery: A Rare Cause of Heart Failure

2015 ◽  
Vol 2015 ◽  
pp. 1-2
Author(s):  
Jagadeesh K. Kalavakunta ◽  
Yashwant Agrawal ◽  
Alicia Williams ◽  
Jerry W. Pratt ◽  
Frank Saltiel
Keyword(s):  
Pulmonary Artery ◽  
Artery Bypass ◽  
Bypass Graft ◽  
Coronary Vessels ◽  
Giant Aneurysm ◽  
Computed Tomographic Angiography ◽  
Venous Graft ◽  
Circumflex Artery ◽  
Left Circumflex Artery ◽  
Computed Tomographic

We report a case of a 74-year-old man who presented with dyspnea on exertion and pedal edema. He had five-vessel coronary artery bypass graft (CABG) surgery twenty-six years ago and redo three-vessel CABG done thirteen years later. Computed tomographic angiography (CTA) of the heart and coronary vessels demonstrated a giant aneurysm arising from the saphenous venous graft (SVG) to the first obtuse marginal of the left circumflex artery compressing the pulmonary artery (PA). He underwent coronary angiography, confirming the CTA findings. Surgical and percutaneous interventions were offered, but the patient opted for conservative management due to the high risk of morbidity and mortality.

scholarly journals P1450 Pulmonary artery sarcoma mimicking as pulmonary thromboembolism for a young man: the role of multimodality imaging for diagnosis

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
R Ereminiene ◽  
E Sakaviciute ◽  
R Ereminas ◽  
A Jankauskas ◽  
L Poskiene ◽  
...  
Keyword(s):  
Respiratory Failure ◽  
Pulmonary Artery ◽  
Ct Scan ◽  
Multimodality Imaging ◽  
Anticoagulation Therapy ◽  
Lower Lobe ◽  
Systolic Pulmonary Artery Pressure ◽  
Pulmonary Artery Sarcoma ◽  
Surgical Specimen ◽  
Laboratory Results

Abstract Patient presentation A 33-year-old man was referred to our hospital suffering fever with shivers, dyspnea, dry cough, and weakness. Initial work up Symptoms appeared three weeks until hospitalization. Laboratory results showed leukocytosis and high levels of inflammatory markers. Haematological diseases were excluded, a chest x-ray showed infiltration in the lower lobe of the right lung, antibiotics were prescribed. Diagnosis and management When clinical and laboratory results showed no signs of improvement, chest computed tomography (CT) scan was performed and bilateral pulmonary artery thromboembolism with right lung infarct-pneumonia was diagnosed (Figure 1, 2). Treatment was supplemented with intravenous anticoagulants. In the course of treatment patient’s status worsened, respiratory failure progressed, so CT scan was performed again and showed massive pulmonary artery thromboembolism without the effect of treatment. Transthoracic 2D echocardiography showed dilated right heart chambers, relative severe tricuspid valve regurgitation, increased systolic pulmonary artery pressure (Video 1, figure 3), pulmonary artery valve masses in the stem which caused obstruction with maximum gradient about 50 mmHg(Video 2, figure 4). For a detailed workup, magnetic resonance imaging (MRI) was done, that revealed tumorous masses from pulmonary artery valve to the pulmonary trunk and right pulmonary branch (Figure 5, 6, 7). The patient underwent pulmoangiography and biopsy was taken out of the masses that suspected sarcoma. The multidisciplinary team came to a conclusion to perform surgery considering worsening patient’s status. The patient underwent pulmonary artery prosthesis implantation and right pneumonectomy (Figure 8). Masses from pulmonary artery valve were examined by pathologists, surgical specimen results showed high grade poorly differentiated pulmonary artery intimal sarcoma (Figure 9, 10). Follow up Early postoperative period was complicated with cardiogenic shock and respiratory failure. Despite extracorporeal membrane oxygenation (ECMO) and high doses of vasopressors patient did not survive the 2nd postoperative day. Conclusions Pulmonary artery sarcoma (PAS) frequently can be misdiagnosed as thromboembolism. Multimodality imaging should be considered pulmonary artery filling defects persist despite proper anticoagulation therapy for early diagnosis and better survival. Abstract P1450 Figure 3.

Case 166: Metastatic Left Pulmonary Artery Sarcoma

Radiology ◽  
2011 ◽  
Vol 258 (2) ◽  
pp. 645-648 ◽  
Author(s):  
Erik S. Mittra ◽  
Andrei H. Iagaru ◽  
Ann N. Leung
Keyword(s):  
Pulmonary Artery ◽  
Left Pulmonary Artery ◽  
Pulmonary Artery Sarcoma

scholarly journals Primary Pulmonary Artery Sarcoma Confined to the Left Pulmonary Artery

2021 ◽  
Vol 9 ◽  
pp. 232470962110146
Author(s):  
Ellery Altshuler ◽  
Grant Lowther ◽  
Michael Jantz
Keyword(s):  
Pulmonary Artery ◽  
Fibrous Histiocytoma ◽  
Correct Diagnosis ◽  
Left Lung ◽  
Left Pulmonary Artery ◽  
Disease Recurrence ◽  
Pulmonary Artery Sarcoma ◽  
Radiographic Findings ◽  
Undifferentiated Sarcoma ◽  
Primary Pulmonary Artery Sarcoma

Primary pulmonary artery sarcomas (PPAS) are extremely rare tumors that are often mislabeled as pulmonary emboli (PE). PPAS usually involve the pulmonary trunk and are histologically classified as leiomyosarcoma, spindle cells sarcoma, fibrous histiocytoma, or undifferentiated sarcoma. Our case involved a 78-year-old man with an undifferentiated PPAS confined to the left pulmonary artery that was initially misdiagnosed as a PE. After a month-long delay in treatment in which the patient was prescribed warfarin, the correct diagnosis was made. Pulmonary artery endarterectomy and left lung pneumonectomy were performed, and he survived for 18 months before disease recurrence and death. Our case helps illustrate some of the clinical and radiographic findings that help distinguish PPAS from PE.

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