scholarly journals Immunoglobulin G4-related disease presenting with pulmonary manifestations, lymphadenopathy, and vocal cord immobility: an unusual presentation of a rare disease

2022 ◽  
Vol 71 (1) ◽  
pp. 135
Author(s):  
Parul Mrigpuri ◽  
Balakrishnan Menon ◽  
Sonam Spalgais ◽  
Ritu Kulshrestha ◽  
Himanshu Saini ◽  
...  
Keyword(s):  
Rare Disease ◽  
Vocal Cord ◽  
Unusual Presentation ◽  
Immunoglobulin G4 ◽  
Related Disease ◽  
Pulmonary Manifestations

scholarly journals Immunoglobulin G4‐related disease: a rare disease with an unusual presentation

2016 ◽  
Vol 4 (7) ◽  
pp. 657-660
Author(s):  
Muhammad Waqas Khan ◽  
Terrance Hadley ◽  
Melissa Kesler ◽  
Zartash Gul
Keyword(s):  
Rare Disease ◽  
Unusual Presentation ◽  
Immunoglobulin G4 ◽  
Related Disease

scholarly journals Unusual Presentation of Immunoglobulin G4-Related Disease: A Case Report

2020 ◽  
Author(s):  
Gözde ZEYBEK ◽  
Sevinç KALIN ◽  
Burcu KARAKAYALI ◽  
Ebru ZEMHERİ ◽  
Sait NADERİ ◽  
...  
Keyword(s):  
Case Report ◽  
Unusual Presentation ◽  
Immunoglobulin G4 ◽  
Related Disease

scholarly journals Pleomorphic Pulmonary Manifestations of IgG4-Related Disease

2019 ◽  
Vol 2019 ◽  
pp. 1-4
Author(s):  
Srikanth Naramala ◽  
Sharmi Biswas ◽  
Sreedhar Adapa ◽  
Vijay Gayam ◽  
Romeo C. Castillo ◽  
...  
Keyword(s):  
Human Body ◽  
Plasma Cells ◽  
Clear Picture ◽  
Lung Involvement ◽  
Immunoglobulin G4 ◽  
Related Disease ◽  
Igg4 Related Disease ◽  
Pulmonary Manifestations ◽  
Sclerosing Pancreatitis

Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis. Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma cells. Involvement of lungs with IgG4 is reported previously, but still, there is no clear picture of the pathophysiology behind lung involvement. Here, we are presenting a patient who has IgG4-RD presenting as pseudotumor of the lungs.

FDG PET/CT in Isolated Mediastinal Immunoglobulin G4–Related Disease

2020 ◽  
Vol 45 (4) ◽  
pp. e195-e197
Author(s):  
Vankadari Kousik ◽  
Rajender Kumar ◽  
Bhagwant Rai Mittal ◽  
Divya Aggarwal ◽  
Ashutosh Nath Aggarwal
Keyword(s):  
Fdg Pet ◽  
Immunoglobulin G4 ◽  
Related Disease ◽  
Pet Ct ◽  
Fdg Pet Ct

scholarly journals Evaluate the Differences in CT Features and Serum IgG4 Levels between Lymphoma and Immunoglobulin G4-Related Disease of the Orbit

2020 ◽  
Vol 9 (8) ◽  
pp. 2425
Author(s):  
Wei-Hsin Yuan ◽  
Anna Fen-Yau Li ◽  
Shu-Yi Yu ◽  
Ying-Yuan Chen ◽  
Chia-Hung Wu ◽  
...  
Keyword(s):  
Elevated Serum ◽  
Hounsfield Unit ◽  
Immunoglobulin G4 ◽  
Related Disease ◽  
Serum Igg4 ◽  
Orbital Lymphoma ◽  
Serum Igg Levels ◽  
Igg Level ◽  
Ct Features ◽  
Higher Sensitivity

Background: Benign immunoglobulin G4 (IgG4)-related orbital disease (IgG4-ROD)—characterized as tumors mimicking malignant orbital lymphoma (OL)—responds well to steroids, instead of chemotherapy, radiotherapy and/or surgery of OL. The objective of this study was to report the differences in computed tomography (CT) features and- serum IgG4 levels of IgG4-ROD and OL. Methods: This study retrieved records for patients with OL and IgG4-ROD from a pathology database during an eight-year-and-five-month period. We assessed the differences between 16 OL patients with 27 lesions and nine IgG4-ROD patients with 20 lesions according to prebiopsy CT features of lesions and prebiopsy serum IgG4 levels and immunoglobulin G (IgG) levels This study also established the receiver-operating curves (ROC) of precontrast and postcontrast CT Hounsfield unit scales (CTHU), serum IgG4 levels, serum IgG levels and their ratios. Results: Significantly related to IgG4-ROD (all p < 0.05) were the presence of lesions with regular borders, presence of multiple lesions—involving both lacrimal glands on CT scans—higher median values of postcontrast CTHU, postcontrast CTHU/precontrast CTHU ratios, serum IgG4 levels and serum IgG4/IgG level ratios. Compared to postcontrast CTHU, serum IgG4 levels had a larger area under the ROC curve (0.847 [95% confidence interval (CI): 0.674–1.000, p = 0.005] vs. 0.766 [95% CI: 0.615–0.917, p = 0.002]), higher sensitivity (0.889 [95% CI: 0.518–0.997] vs. 0.75 [95% CI: 0.509–0.913]), higher specificity (0.813 [95% CI: 0.544–0.960] vs. 0.778 [95% CI: 0.578–0.914]) and a higher cutoff value (≥132.5 mg/dL [milligrams per deciliter] vs. ≥89.5). Conclusions: IgG4-ROD showed distinct CT features and elevated serum IgG4 (≥132.5 mg/dL), which could help distinguish IgG4-ROD from OL.

Immunoglobulin G4–related disease of the paratestis: Can we avoid radical treatment?

2020 ◽  
pp. 205141582098277
Author(s):  
Thomas Thompson ◽  
Thomas Brophy ◽  
Mohsin Uddin ◽  
James Bolton ◽  
Richard Napier-Hemy
Keyword(s):  
Immunoglobulin G4 ◽  
Related Disease ◽  
Radical Treatment

Sonographic Appearance of the Submandibular Glands in Patients With Immunoglobulin G4-Related Disease

2012 ◽  
Vol 31 (3) ◽  
pp. 489-493 ◽  
Author(s):  
Satomi Asai ◽  
Kenji Okami ◽  
Naoya Nakamura ◽  
Shuichi Shiraishi ◽  
Tomohiro Yamashita ◽  
...  
Keyword(s):  
Immunoglobulin G4 ◽  
Sonographic Appearance ◽  
Submandibular Glands ◽  
Related Disease

AB0917 Pulmonary Manifestations in Patients with IGG4-Related Disease at A Tertiary Care Institute: Table 1.

2016 ◽  
Vol 75 (Suppl 2) ◽  
pp. 1215.3-1215
Author(s):  
R. Banka ◽  
Y. Gc ◽  
C. Balakrishnan ◽  
R. Samant ◽  
L. Pinto ◽  
...  
Keyword(s):  
Tertiary Care ◽  
Related Disease ◽  
Igg4 Related Disease ◽  
Care Institute ◽  
Pulmonary Manifestations

ALK-Positive Inflammatory Myofibroblastic Tumor of the Nipple During Pregnancy-An Unusual Presentation of a Rare Disease

2015 ◽  
Vol 21 (3) ◽  
pp. 297-302 ◽  
Author(s):  
Anikó Kovács ◽  
Gyöngyvér Máthé ◽  
Jan Mattsson ◽  
Göran Stenman ◽  
Lars-Gunnar Kindblom
Keyword(s):  
Rare Disease ◽  
Inflammatory Myofibroblastic Tumor ◽  
Unusual Presentation ◽  
Alk Positive

Immunoglobulin G4–Related Disease Presenting as Bilateral Arthritis of the Hip Joints

2018 ◽  
Vol 24 (7) ◽  
pp. 398-401 ◽  
Author(s):  
Zhongping Zhan ◽  
Minxi Lao ◽  
Zheng Yang ◽  
Dongying Chen ◽  
Xiuyan Yang
Keyword(s):  
Hip Joints ◽  
Immunoglobulin G4 ◽  
Related Disease
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